"biliary atresia splenic malformation: characterised by splenic malformation (polysplenia, asplenia, double spleen) along with variably incidence of situs inversus (in ~40%; intestinal malrotation (~60%), pre-duodenal portal vein (~35%), absent inferior vena cava (~25%)"
"Tc-99m diosgenin (DISIDA) and mebrofenin (BRIDA) have the highest hepatic extraction rate and shortest transit time of hepatobiliary radiotracers. Cases of biliary atresia typically demonstrate relatively good hepatic uptake with no evidence of excretion into the small bowel at 24 hours (unlike in neonatal hepatitis which is a primary differential)."
"Kasai portoenterostomy: the surgery involves exposing the porta hepatis (the area of the liver from which bile should drain) by radical excision of all bile duct tissue up to the liver capsule and attaching a Roux-en-Y loop of jejunum to the exposed liver capsule above the bifurcation of the portal vein creating a portoenterostomy 7"
Expected headings
"Associations"
"Hepatobiliary (HIDA) scan"
"Complications"
"Biliary atresia has a variable global incidence, estimated at 1 in 5000-10,000 live births in Taiwan/Japan and 1 in 15,000-22,000 live births in Europe/North America 9. There is a recognised male predilection."
"biliary atresia splenic malformation: characterised by splenic malformation (polysplenia, asplenia, double spleen) along with variably incidence of situs inversus (in ~40%; intestinal malrotation (~60%), pre-duodenal portal vein (~35%), absent inferior vena cava (~25%)"