"Differential Diagnosis"
Expected headings
"Associations"
"Differential Diagnosis"
"The pathogenesis is poorly understood. The disease is characterised by dense bile duct infiltration by IgG4-positive plasma cells resulting in extensive fibrosis. There are often elevated serum IgG4 levels."
"cholangiocarcinomaconfined to the bile ducts; IgG4 may have other manifestations of disease such as autoimmune pancreatitis"