"It is thought to typically affect children and young adults 8-9."
"Pathologically, PCH is characterised by the proliferation of benign thin-walled capillary-sized blood vessels within the lung parenchyma 5. Proliferating capillaries invade the pulmonary interstitium and alveolar septae and occlude the pulmonary vasculature. Invasion of pulmonary veins and, less frequently, pulmonary arteries can be common 8."
"The natural history of pulmonary capillary haemangiomatosis is one of rapid deterioration 3. Lung or heart-lung transplantation may be the only curative therapeutic option where pharmacologic agents serve only as supportive care and a bridge to transplantation (although treatment with vasodilators will lead to more rapid deterioration) 6. PCH has not been reported to recur after transplantation. There are occasional reports of successful antiangiogenic therapy with Doxycycline 10."