Expected headings
"Pancreatic manifestations"
"Hepatobiliary manifestations"
"Liver parenchymal disease"
"Biliary tree"
"Gastrointestinal manifestations"
"Renal manifestations"
"Abdominal manifestations in cystic fibrosis (CF) are common, varied and nearly all organ systems can be affected, and it should be remembered that only 39% of patients with cystic fibrosis have pulmonary symptoms as their sole complaint 1. Not only that, but 7% of cystic fibrosis patients do not present until adulthood."
"focal biliary cirrhosis (pathognomonic for cystic fibrosis and present in 78%): focal portal fibrosis and cholestasis; thickened hyperechoic periportal tissue on ultrasound (>2 mm thickness)"
"hepatic steatosis (23-67% 6; seen in 30% of cystic fibrosis patients at biopsy, 30-50% at imaging and 60% at autopsy 2)"
"intussusception: typically ileocolic and may result from adherent faecal residue or enlarged lymphoid follicles 4; a chronically distended appendix may be the lead point"