"Chronic thromboembolic pulmonary hypertension is a rare disease. The exact prevalence and annual incidence of CTEPH are unknown. Data from the United Kingdom suggest that CTEPH may occur in approximately five individuals per million population per year 2. A cumulative incidence of 0.1–9.1% within the first two years after an episode of symptomatic pulmonary embolus (PE) has been reported 3. However, some patients develop CTEPH in the absence of symptoms of previous acute PE 4."
"Surgical resectability can be classified according to the University of California, San Diego (UCSD)-CTEPH surgical classification, and is a useful clinical addition to a report impression 9."
Expected headings
"Pulmonary arteries"
"Pulmonary veins"
"Heart"
"Lung"
"Classification"
"Clinical symptoms and signs are non-specific or absent in early stage of the disease, the impact of right heart failure only becomes evident in advanced disease. When present, the symptoms of CTEPH may resemble those of acute pulmonary embolism, idiopathic pulmonary arterial hypertension, asthma or chronic obstructive pulmonary disease 1,5. The non-specificity of symptoms and signs may contribute to a delay in diagnosis, often up to three years."
"intraluminal fibrous webs or bands, these appear as linear intraluminal filling defects; intraluminal fibrous bands are ribbon-like structures anchored to the vessel wall at two points with a free mid-portion (often orientated along the long axis of vessel) while intraluminal fibrous webs are branching networks of bands"