"Echocardiography/ultrasound "
"Diagnosis relies on visualisation of the septal leaflet of the tricuspid valve, typically appreciated from transthoracic parasternal and apical windows. Apical displacement of the septal leaflet in excess of 8 mm per m2 (body surface area) with “sail-like” elongation is considered diagnostic 12. Further features include:"
"abnormal PR interval"
"alternatively, may demonstrate a prolonged PR interval"
"multiple other congenital heart lesions (ASD is quite common)"
"If you find Ebstein anomaly, also look for other associated defects: right ventricular outflow tract (RVOT) abnormalities, ASD (especially ostium secundum type), VSD, and tetralogy of Fallot."
"In your report, mention the position of tricuspid valve leaflets, assess the degree of regurgitation, and measure right ventricular volume and function. Be sure that you quote "true" RV volume (volume of the ventricular side of the tricuspid valve)."
"Uhl anomaly 3"
Expected headings
"ECG"
"Associations"
"Echocardiography/ultrasound "
"The anomaly accounts for only ~0.5% of congenital cardiac defects 6,7, although it is the most common cause of congenital tricuspid regurgitation. There is no recognised gender predilection, and almost all cases seem to be sporadic, although an association with maternal lithium carbonate injection has been postulated 6. A few familial cases have been reported 6,7."
"There is often severe right-sided cardiomegaly due to an elongated and enlarged right atrium, which may result in an elevated apex. Classically, the heart is described as having a "box shape" on a frontal chest radiograph."
"History and etymology"