"MRI may show fatty infiltration in the right ventricle (and occasionally in the left ventricle) 8, but this can also be seen in normal myocardium 3 and is no longer part of the diagnostic criteria 9. A corrugated pattern to the right ventricular wall may be seen, known as the “accordion sign.”"
"localised widening of QRS complex (V1-3)"
"usually regular, wide (QRS duration >120 ms) complex rhythms with rates between 140-250 beats per minute"
"deviation of the QRS axis in the frontal plane"
"often demonstrates a morphology consistent with an ectopic origin in the right ventricular outflow tract (RVOT VT)"
"major QRS vector travels from the base to the apex, roughly leftward and inferiorly, thus appearing predominantly positive in leads aVL (high lateral) and II, III and aVF (inferior)"
"regional RV akinesia or dyskinesia or dyssynchronous RV contraction and 1 of the following:"
"regional RV akinesia or dyskinesia or dyssynchronous RV contraction and 1 of the following:"
"ratio of RV end-diastolic volume to BSA (body surface area) ≥110 mL/m2 (male) or ≥100 mL/m2 (female)"
"RV ejection fraction ≤40%"
"regional RV akinesia or dyskinesia or dyssynchronous RV contraction and 1 of the following:"
"regional RV akinesia or dyskinesia or dyssynchronous RV contraction and 1 of the following:"
"ratio of RV end-diastolic volume to BSA ≥100 to"
"RV ejection fraction >40% to ≤45%"
"usually regular, wide (QRS duration >120 ms) complex rhythms with rates between 140-250 beats per minute"
"a fractional area change between 34-39%"
"Echocardiography has inconsistent sensitivity and specificity for the diagnosis of ARVC and is not considered a primary modality in the final diagnosis 12."
"Uhl anomaly"
"Ebstein anomaly"
Expected headings
"ECG"
"Associations"
"Echocardiography"
"The estimated population prevalence is thought to range around 1 in 1000-5000 8. It typically presents in young individuals. There is a recognised male predilection, with a male-to-female ratio of 2.7:1. Several reports suggest that there is a familial occurrence of ARVC of about 30-50%, with mainly autosomal dominant inheritance, variable penetrance, and polymorphic phenotypic expression."
"major QRS vector travels from the base to the apex, roughly leftward and inferiorly, thus appearing predominantly positive in leads aVL (high lateral) and II, III and aVF (inferior)"