"cystic: type 1 (prenatal and 10 months old), 14%"
"mixed: type 2 (mean age 34 months), 48%"
"solid: type 3 (mean age 44 months), 38%"
"type 1: lesions manifest as a single cyst or a multicystic lesion (often air-filled)"
"type 2: lesions show air- or fluid-filled cavities with possible air-fluid levels along with solid internal nodules"
"type 3: neoplasms are solid lesions that show low attenuation at CT and homogeneous or heterogeneous enhancement"
"Type 3 pleuropulmonary blastoma shows increased 18F-fluorodeoxyglucose (FDG) uptake at PET-CT 13"
"Pleuropulmonary blastoma is encountered in childhood, mostly in the first years of life (90% in those between 0-2 years old)."
"Pleuropulmonary blastoma is associated with PPB family tumour and dysplasia syndrome in 33% of cases. Many of these patients have a mutation of the DICER1 gene. In 10% of cases, patients with PPB may also present with multilocular cystic nephroma, and, very rarely, Wilms tumour 7-9."
"Pleuropulmonary blastoma is associated with PPB family tumour and dysplasia syndrome in 33% of cases. Many of these patients have a mutation of the DICER1 gene. In 10% of cases, patients with PPB may also present with multilocular cystic nephroma, and, very rarely, Wilms tumour 7-9."
"types 1 and 4 CPAM: indistinguishable from type 1 pleuropulmonary blastoma; however, congenital lung malformations are often detected during the second trimester fetal US, whereas PPB are usually discovered postnatally 13"
"types 1 and 4 CPAM: indistinguishable from type 1 pleuropulmonary blastoma; however, congenital lung malformations are often detected during the second trimester fetal US, whereas PPB are usually discovered postnatally 13"
"Pleuropulmonary blastoma is associated with PPB family tumour and dysplasia syndrome in 33% of cases. Many of these patients have a mutation of the DICER1 gene. In 10% of cases, patients with PPB may also present with multilocular cystic nephroma, and, very rarely, Wilms tumour 7-9."
"primitive neuroectodermal tumour (PNET) of the thorax"
Expected headings
"Associations"
"PET-CT"
"types 1 and 4 CPAM: indistinguishable from type 1 pleuropulmonary blastoma; however, congenital lung malformations are often detected during the second trimester fetal US, whereas PPB are usually discovered postnatally 13"