"Treatment consists of radical nephrectomy and resection of adjacent lymph nodes followed by chemotherapy. Survival is poor, with an 18-month survival rate of only 20%, and almost all patients succumbing before 5 years post-diagnosis 1,2."
"Rhabdoid tumour of the kidney is a rare, highly aggressive malignancy of early childhood, closely related to atypical teratoid/rhabdoid tumours (AT/RT) of the brain (see rhabdoid tumours)."
"Rhabdoid tumour of the kidney is a rare, highly aggressive malignancy of early childhood, closely related to atypical teratoid/rhabdoid tumours (AT/RT) of the brain (see rhabdoid tumours)."
"Rhabdoid tumours have the worst prognosis of all renal tumours. It is highly aggressive and metastasises early, with up to 80% of patients presenting with metastatic disease, typically to the lungs and less often to the liver, abdomen, brain, lymph nodes, or skeleton 1,2."