"Both ocular and orbital involvement in GPA has been reported in 40-50% of patients 1-3. Ophthalmologic disease occasionally can be the initial clinical manifestation in the limited form of granulomatosis with polyangiitis 2."
"Clinical presentation "
"Granulomatosis with polyangiitis (previously known as Wegener granulomatosis), is a multi-system systemic necrotising non-caseating granulomatous vasculitis affecting small to medium-sized arteries, capillaries and veins."
"granulomatous disease causing an orbital inflammatory mass, often with proptosis and/or optic nerve compression"
"small-vessel vasculitis causing conjunctivitis, scleritis, episcleritis, uveitis, optic neuritis, optic nerve vasculitis, or retinitis 2,4"
Expected headings
"Clinical presentation "
"Granulomatosis with polyangiitis (previously known as Wegener granulomatosis), is a multi-system systemic necrotising non-caseating granulomatous vasculitis affecting small to medium-sized arteries, capillaries and veins."
"small-vessel vasculitis causing conjunctivitis, scleritis, episcleritis, uveitis, optic neuritis, optic nerve vasculitis, or retinitis 2,4"